Haily Haily disease

Haily Haily Disease

Remember as AFB Die at High Temp

A- Autosomal dominant
F- Flaccid vescicle on flexures, Family history
positive
B- Benign familial chronic pemphigus
Die- Decreased desmosomes (Pathology)
High- History of multiple relapse & remissin (Characteristic)
Temp- Third- fourth decade (Age of presentation)

Printed from RxPG
http://www.rxpgonline.com